Cerebellar Disorders in Children – Chapter 4: Impairments of Cognition and Emotion in Children with Cerebellar Disorders (ebook)


Chapter 4 – Impairments of Cognition and Emotion in Children with Cerebellar Disorders: An Approach to Recognition, Evaluation and Treatment

Jeremy D. Schmahmann, Annah N. Abrams, and Janet C. Sherman

The clinical neurology of the cerebellum has evolved dramatically in recent years. We recognize the traditional clinical phenomenology of the cerebellar motor syndrome characterized by impairments of gait, extremity coordination, speech and oculomotor control, as discussed in Chapter 3. In addition, however, and of particular relevance to the developing nervous system, is the new field of the cognitive neuroscience of the cerebellum that has implications for diagnosis and management of children with cerebellar disorders. In this chapter we briefly review the evolution of ideas about the functions of the cerebellum, describe the neurobehavioral features that have been reported in pediatric patients with cerebellar diseases, and present an approach to the evaluation and management of these cases.

Please note that Chapters 2, 3 and 4 are also available in Part 2: Cerebellar Anatomy and Functions.

About the Complete Book:

This clinically orientated text by an international group of experts is the first definitive reference book on disorders of the cerebellum in children. It presents a wealth of practical clinical experience backed up by a strong scientific basis for the information and guidance given. The first part sets out the theoretical underpinnings of cerebellar disorders. This is followed by sections on clinical conditions grouped according to common characteristics such as aetiology and symptomatology. The descriptions of the clinical conditions each systematically cover, as appropriate, epidemiology, prevalence, diagnostic criteria, clinical features (including course and prognosis), pathophysiology, genetics, investigations, differential diagnosis, and management and treatment. This book will be an invaluable resource for all those caring for children affected by cerebellar disorders, including malformations, genetic and metabolic disorders, acquired cerebellar damage, vascular disorders and acute ataxias. This comprehensive reference text on cerebellar disorders in children includes chapters on cerebellar development, prenatal cerebellar imaging, imaging of the posterior fossa, with coverage of a broad range of malformations, genetic and metabolic disorders involving the cerebellum, prenatal cerebellar disruptions (as related to prematurity), vascular disorders, tumors and paraneoplastic syndromes, as well as acute ataxia and trauma to the posterior fossa. Numerous checklists are provided to assist in the differential diagnosis of clinical signs and neuroimaging findings.

Paediatric neurologists, paediatricians, neurologists, developmental paediatricians, neuroimaging specialists, geneticists, neonatologists

Clinics in Developmental Medicine No. 191-192